Anaesthesia for Caesarean Section in a Patient With Familial Amyloid Polyneuropathy Type I

Familial amyloid polyneuropathy type I is a rare neurodegenerative disease characterised by early-onset and progressive peripheral sensorimotor and autonomic polyneuropathy. A pregnant woman with familial amyloid polyneuropathy type I presented with mild gastrointestinal, cardiac involvement and peripheral neuropathy, aggravated during the pregnancy. The caesarean delivery was performed under uneventful epidural anaesthesia. Anaesthesia of a pregnant woman with this condition can be challenging due to its multisystemic involvement and the possibility of further neurologic injury. This is one of the few cases of anaesthesia for caesarean section described in familial amyloid polyneuropathy type I patients. Given the possibility of similar cases, it is essential to disclose the anaesthetic management.