Electrophysiological Phenotype-Genotype Study of Sustained Monomorphic Ventricular Tachycardia in Inherited, High Arrhythmic Risk, Left Ventricular Cardiomyopathy
The anatomic substrate of SMVTs shows a strong correlation with the underlying genotype, electrocardiographic morphology, and recurrence rate. Particularly, patients with nuclear membrane gene variants have a significantly higher recurrence rate compared with those with desmosomal gene variants.
Authors
- Sara Vázquez‐Calvo (ORCID: https://orcid.org/0000-0002-3787-6853)
- Roberto Barriales‐Villa (ORCID: https://orcid.org/0000-0002-6721-3487)
- Perry Elliott (ORCID: https://orcid.org/0000-0003-3383-3984)
- Nerea Mora Ayestarán (ORCID: https://orcid.org/0000-0002-2127-5287)
- William J. McKenna (ORCID: https://orcid.org/0000-0001-7994-2460)
- Esther Zorio (ORCID: https://orcid.org/0000-0003-3608-4210)
- Víctor Castro‐Urda (ORCID: https://orcid.org/0000-0002-8325-1379)
- Julia Martínez Solé (ORCID: https://orcid.org/0000-0001-8084-3531)
- Alessio Gasperetti (ORCID: https://orcid.org/0000-0003-3432-070X)
- Giovanni Peretto (ORCID: https://orcid.org/0000-0003-1815-4000)
- Francisco Bermúdez-Jiménez (ORCID: https://orcid.org/0000-0003-0325-7349)
- Pier D. Lambiase (ORCID: https://orcid.org/0000-0002-9055-9267)
- Rosa Macías‐Ruiz (ORCID: https://orcid.org/0000-0003-4686-5678)
- Ardan M. Saguner (ORCID: https://orcid.org/0000-0003-1896-0803)
- Eva Cabrera‐Borrego (ORCID: https://orcid.org/0000-0003-2997-2391)
- Luís R. Lopes (ORCID: https://orcid.org/0000-0002-6408-4667)
- Miguel Álvarez (ORCID: https://orcid.org/0000-0002-0909-0749)
- Paolo Compagnucci (ORCID: https://orcid.org/0000-0003-1924-6548)
- Juan Jiménez‐Jáimez (ORCID: https://orcid.org/0000-0001-5541-898X)
- José M. Larrañaga‐Moreira (ORCID: https://orcid.org/0000-0003-4642-4098)
- Pablo Fernández de‐Aspe (ORCID: https://orcid.org/0000-0002-2676-8507)
- Sebastián Giacoman
- Ivo Roca‐Luque (ORCID: https://orcid.org/0000-0003-0731-3731)
- Claudio Tondo (ORCID: https://orcid.org/0000-0002-8500-8313)
- Harikrishna Tandri (ORCID: https://orcid.org/0000-0003-2651-4352)
- Pablo Sánchez‐Millán (ORCID: https://orcid.org/0000-0001-6863-2715)
- Michela Casella (ORCID: https://orcid.org/0000-0002-5322-1742)
- Victoria Cañadas‐Godoy (ORCID: https://orcid.org/0000-0003-2312-8288)
- Johanna Tonko (ORCID: https://orcid.org/0000-0002-4689-8384)
- Petr Peichl (ORCID: https://orcid.org/0000-0002-5625-0071)
- Luís Tercedor (ORCID: https://orcid.org/0000-0002-9566-8809)
- Carmen Muñoz‐Esparza (ORCID: https://orcid.org/0000-0001-8656-244X)
- Manuel Molina‐Lerma (ORCID: https://orcid.org/0000-0002-3988-6721)
- Moisés Rodríguez‐Mañero (ORCID: https://orcid.org/0000-0001-7566-9321)
- Elena Paiotti
Institutions
- Johns Hopkins University (US)
- Vita-Salute San Raffaele University (IT)
- Universidad de Granada (ES)
- Vanderbilt University (US)
- Cardiovascular Institute of the South (US)
- Johns Hopkins Medicine (US)
- Hospital Clínico San Carlos (ES)
- Hospital Universitari i Politècnic La Fe (ES)
- British Heart Foundation (GB)
- Centro Cardiologico Monzino (IT)
- Instituto de Investigación Sanitaria del Hospital Clínico San Carlos (ES)
- University Hospital of Zurich (CH)
- Hospital Universitario Puerta de Hierro Majadahonda (ES)
- Zurich Heart House (CH)
- Hospital Santiago Apostol (ES)
- Instituto de Investigación Biosanitaria de Granada (ES)
- Centro de Investigación Biomédica en Red (ES)
- Hospital Clínic de Barcelona (ES)
- Institute of Clinical and Experimental Medicine (CZ)
- Complexo Hospitalario Universitario A Coruña (ES)
- Hospital Universitario Virgen de la Arrixaca (ES)
- Instituto de Investigación Biomédica de A Coruña (ES)
- Vanderbilt Health (US)
- Ospedali Riuniti Umberto I (IT)
- Instituto de Investigación Sanitaria La Fe (ES)
- University College London (GB)
- University of Baltimore (US)
- Vanderbilt University Medical Center (US)
Publication Details
- Journal
- Circulation Arrhythmia and Electrophysiology
- Published
- 2024-11-29
- DOI
- https://doi.org/10.1161/circep.124.013145
- Citations
- 6
- Primary Topic
- Cardiomyopathy and Myosin Studies
- Type
- article
- Field-Weighted Citation Impact
- 2.41