Rare Encounter Behind the Ear: Unveiling Kimura Disease in the Postaural Region

Abstract Introduction: Kimura disease, a rare chronic inflammatory disorder primarily impacting subcutaneous tissue, particularly affects young Asian males, with around 200 reported cases in India. Its etiology, linked to an abnormal allergic reaction, remains uncertain, featuring a characteristic indolent growth pattern. The condition manifests as swelling and lesions in the head and neck region, involving subcutaneous soft tissue, major salivary glands, and lymph nodes. Eosinophilia and elevated serum immunoglobulin E levels are common, and diagnosis relies on biopsy. Given its benign nature, optimal management lacks consensus. Case Report: Presented is a case of Kimura disease in the postauricular region, treated with surgical excision under local anesthesia. Post-operative steroid therapy resulted in an absence of recurrence and reduced eosinophilia during follow-up. Discussion: Managing Kimura disease is challenging due to its rarity and diverse clinical presentations. Treatment options encompass systemic steroids, antihistamines, immunosuppressants, chemotherapy, radiotherapy, and surgical excision. Despite interventions, the disease often locally recurs. Our case highlights the efficacy of surgical excision under local anesthesia, coupled with post-operative steroids, in preventing recurrence and reducing eosinophilia. Ongoing research and case reports are crucial for establishing standardized protocols in Kimura disease management. KEYWORDS: Kimura disease; postauricular region; eosinophilia; surgical excision