Percorsi diagnostico-terapeutici assistenziali per i pazienti con amiloidosi cardiaca – Documento di consenso SIC/ANMCO. A cura della Rete Italiana dell’Amiloidosi Cardiaca (RIAC)

The perspective on cardiac amyloidosis has deeply changed over the last 10 years following major advances in diagnosis and treatment options. This heterogeneous disease requires the interaction among experts of different specialties and subspecialties. Suspicion of disease, timely recognition and confirmation of final diagnosis, prognostic stratification, overall management and therapeutic strategies represent ongoing challenges in the clinical setting. Missing or delayed diagnosis may have significant impact on patient outcome, especially in light-chain amyloidosis. The present inter-society consensus document aims to provide a standardized approach to the diagnosis of cardiac amyloidosis in Italy, and to discuss the challenging clinical scenarios encountered in routine activity for cardiologists and physicians of different specialties dealing with patients with suspected or established cardiac amyloidosis. This document may be adapted to the setting of each specific region.

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Publication Details

Journal
Giornale italiano di cardiologia
Published
2024-12-01
DOI
https://doi.org/10.1714/4372.43703
Citations
4
Primary Topic
Amyloidosis: Diagnosis, Treatment, Outcomes
Type
article
Field-Weighted Citation Impact
0.94
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article

Percorsi diagnostico-terapeutici assistenziali per i pazienti con amiloidosi cardiaca – Documento di consenso SIC/ANMCO. A cura della Rete Italiana dell’Amiloidosi Cardiaca (RIAC)

Matteo Serenelli, Marco Merlo, Massimo Grimaldi, Stefano Perlini et al.
4 citations
Giornale italiano di cardiologia
Amyloidosis: Diagnosis, Treatment, Outcomes
0.94
article

Percorsi diagnostico-terapeutici assistenziali per i pazienti con amiloidosi cardiaca – Documento di consenso SIC/ANMCO. A cura della Rete Italiana dell’Amiloidosi Cardiaca (RIAC)

Matteo Serenelli, Marco Merlo, Massimo Grimaldi, Stefano Perlini, Alberto Cipriani, Simone Longhi, Fabrizio Oliva, Beatrice Musumeci, Fabio Vagnarelli, Michele Emdin, Gianfranco Sinagra, Gianluca Di Bella, Giuseppe Vergaro, Cristina Chimenti, Federico Perfetto, Cinzia Forleo, Giuseppe Limongelli, Massimo Imazio, Massimo Iacoviello, Furio Colivicchi, Daniela Tomasoni, Ciro Indolfi, Laura Piera Obici, Aldostefano Porcari, Marco Canepa, Francesco Cappelli, Giovanni O. Palladini, Giampaolo Merlini, Pasquale Perrone Filardi, Alberto Aimo, Francesco Musca, Marco Metra, Andrea Di Lenarda
article en
4 citations

Abstract

The perspective on cardiac amyloidosis has deeply changed over the last 10 years following major advances in diagnosis and treatment options. This heterogeneous disease requires the interaction among experts of different specialties and subspecialties. Suspicion of disease, timely recognition and confirmation of final diagnosis, prognostic stratification, overall management and therapeutic strategies represent ongoing challenges in the clinical setting. Missing or delayed diagnosis may have significant impact on patient outcome, especially in light-chain amyloidosis. The present inter-society consensus document aims to provide a standardized approach to the diagnosis of cardiac amyloidosis in Italy, and to discuss the challenging clinical scenarios encountered in routine activity for cardiologists and physicians of different specialties dealing with patients with suspected or established cardiac amyloidosis. This document may be adapted to the setting of each specific region.

Giornale italiano di cardiologiaVol. 25(12)
University of Messina (IT), Scuola Superiore Sant'Anna (IT), University of Ferrara (IT), University of Pavia (IT), Policlinico Umberto I (IT), Regione Campania (IT), Magna Graecia University (IT), Ospedali Riuniti di Foggia (IT), Società Italiana di Cardiologia (IT), Azienda Socio Sanitaria Territoriale Grande Ospedale Metropolitano Niguarda (IT), Azienda Universitaria Ospedaliera Consorziale - Policlinico Bari (IT), Ospedale San Filippo Neri (IT), Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia (IT), Presidio Ospedaliero (IT), Ospedale Santa Maria della Misericordia di Udine (IT), University of Campania "Luigi Vanvitelli" (IT), ERN GUARD-Heart (NL), Ospedale Generale Regionale Francesco Miulli (IT), Ospedale Policlinico San Martino (IT), Policlinico San Matteo Fondazione (IT), Fondazione Toscana Gabriele Monasterio (IT), Azienda Sanitaria Universitaria Integrata di Trieste (IT), Ospedali Riuniti Umberto I (IT), University of Bari Aldo Moro (IT), Sapienza University of Rome (IT)
Openalex Percentile: Top 24%
Amyloidosis: Diagnosis, Treatment, Outcomes
0.94
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