Pulmonary lymphangiomatosis: insights into an ultra-rare disease
This case series illustrates the variability of the clinical presentation of PL. Among our patients, those treated with sirolimus showed significant clinical, functional and radiological improvement. However, further investigation is needed to understand the pathogenesis of lymphangiomatosis in order to establish therapeutic approaches.
Authors
- Markus Polke (ORCID: https://orcid.org/0000-0002-9498-7066)
- Michael Kreuter (ORCID: https://orcid.org/0000-0003-4402-2159)
- Lutz Frankenstein (ORCID: https://orcid.org/0000-0001-7216-1004)
- Katharina Buschulte (ORCID: https://orcid.org/0000-0002-7598-5276)
- Felix Herth (ORCID: https://orcid.org/0000-0002-7638-2506)
- Nilab Polke
- Stella Piel
- Claus Peter Heußel (ORCID: https://orcid.org/0000-0001-5809-5733)
- Julia Wälscher
- Martin Eichhorn (ORCID: https://orcid.org/0000-0002-0362-0374)
- Eva Brunnemer
- Monika Eichinger
- Skaidrius Miliauskas (ORCID: https://orcid.org/0009-0002-6130-0712)
- Arne Warth
Institutions
- Lithuanian University of Health Sciences (LT)
- Johannes Gutenberg University Mainz (DE)
- Heidelberg University (DE)
- University Hospital Heidelberg (DE)
- Ruhrlandklinik (DE)
- University Medical Center of the Johannes Gutenberg University Mainz (DE)
- Frauenklinik Heidelberg (DE)
- German Center for Lung Research (DE)
- Pulmonary Associates (US)
Publication Details
- Journal
- Respiratory Research
- Published
- 2024-11-26
- DOI
- https://doi.org/10.1186/s12931-024-03040-5
- Citations
- 3
- Primary Topic
- Vascular Malformations and Hemangiomas
- Type
- article
- Field-Weighted Citation Impact
- 1.72