Navigating Complexity

Anomalous pulmonary venous connections represent a heterogeneous group of congenital heart diseases in which a part or all of the pulmonary veins drains into the right atrium instead of draining into the left atrium. pulmonary veinous anomalies can manifest as partial or total anomalous drainage due to the abnormal embryological development. Multidetector-CT angiography, with its multiplanar reformatting and volume rendering techniques, precisely offers the information about the three-dimensional anatomy and spatial relationships of the cardiovascular structures. Clinical features of anomalous pulmonary venous connections may be silent or have variable features like neonatal cyanosis, volume overload, and pulmonary arterial hypertension due to the left-to-right shunt, which are often associated with other congenital cardiac disease , so that accurate diagnosis is essential for treatment planning