A Rare Surgical Case of Isolated Double-Chambered Right Ventricle Without Cardiac Malformations in an Older Female Patient

Double-chambered right ventricle (DCRV) is a congenital heart disease. Most cases of DCRV are complicated by another congenital cardiac anomaly. Mostly, a ventricular septal defect (VSD) is the usual comorbidity. The flow turbulence by VSD has been suggested to be associated with DCRV, which occurs in many patients during childhood, but very rarely in later years of life. Although there are some cases of DCRV in older adults, there is almost no literature on patients over 70 years of age. We report the surgical case of a 72-year-old female patient with isolated DCRV who visited the hospital due to fatigue. Transthoracic echocardiography (TTE) revealed severe right heart overload, severe tricuspid valve regurgitation, and right ventriculography, leading to a diagnosis of DCRV. We resected anomalous muscle bundles caused by right ventricular outflow tract (RVOT) stenosis via the transventricular approach, closed RVOT using a bovine pericardium patch, and performed tricuspid annuloplasty. Intraoperative findings showed no VSD. After surgery, right ventricular pressure decreased significantly, the patient was discharged on postoperative day 20. DCRV is one of the pathological conditions of which prognosis can be improved with appropriate surgical intervention even in advanced age.