RV-PA uncoupling is associated with increased mortality in transthyretin amyloid cardiomyopathy treated with tafamidis
Impaired adaptation of the RV to increased afterload is associated with worse outcome in ATTR-CM patients. RV-PAc ratio can serve as an echocardiographic predictor for all-cause mortality. Therefore, the determination of RV-PAc could improve risk stratification for ATTR-CM patients.
Authors
- Steffen Maßberg (ORCID: https://orcid.org/0000-0001-7387-3986)
- Norbert Frey (ORCID: https://orcid.org/0000-0001-7611-378X)
- Stefan Kääb (ORCID: https://orcid.org/0000-0001-8824-3581)
- Yavor Metodiev (ORCID: https://orcid.org/0000-0003-0347-4693)
- Stéphanie Kristina Schwarting (ORCID: https://orcid.org/0000-0001-5954-5695)
- Stefan Schönland (ORCID: https://orcid.org/0000-0002-4853-5579)
- Eva Hofmann
- Fabian aus dem Siepen (ORCID: https://orcid.org/0000-0003-4264-1722)
- Lukas Stolz (ORCID: https://orcid.org/0000-0002-1362-1493)
- Michael Poledniczek (ORCID: https://orcid.org/0000-0002-6091-9823)
- Ute Hegenbart (ORCID: https://orcid.org/0000-0003-1917-6746)
Institutions
- Heidelberg University (DE)
- University Hospital Heidelberg (DE)
- LMU Klinikum (DE)
- ERN GUARD-Heart (NL)
- Medical University of Vienna (AT)
- Ludwig-Maximilians-Universität München (DE)
Publication Details
- Journal
- Clinical Research in Cardiology
- Published
- 2024-11-20
- DOI
- https://doi.org/10.1007/s00392-024-02576-2
- Citations
- 5
- Primary Topic
- Amyloidosis: Diagnosis, Treatment, Outcomes
- Type
- article
- Field-Weighted Citation Impact
- 1.17