Retroperitoneal Teratoma: A Rare Entity in a Young Infant

Abstract Background: Primary retroperitoneal teratoma of infancy is rare, comprising only 3.5%–4% of all germ cell tumors. The presentation may range from an asymptomatic mass to an abdominal lump causing symptoms due to mass effect on the neighbouring organs. We present a young infant with an abdominal mass who posed a diagnostic challenge. Clinical Description: A 3monthold female infant with an uneventful antenatal and perinatal history presented with complaints of abdominal distension since 1½ months of age. A lump was palpable involving the entire right side of the abdomen, crossing the midline. Management and Outcome: Despite detailed radiological imaging and trucut biopsy, the diagnosis was unclear. A complete open laparoscopic excision of the mass followed by a biopsy confirmed the diagnosis of grade 2/3 immature teratoma. Serum alphafetoprotein levels and betahuman chorionic gonadotropin levels were normal. Chemotherapy was not administered. The patient has been on followup for the past 2½ years, doing well without any complaints. Conclusion: Early recognition and complete excision of primary retroperitoneal teratoma with mature or partly immature histopathology carries a good prognosis.