Desmoplakin Cardiomyopathy in Pediatric Patients: A Distinct, Underrecognized Cohort of Arrhythmogenic Cardiomyopathy
<i>DSP</i> cardiomyopathy in children and adolescents has varied phenotypic manifestations based on age and genotype and often can be diagnosed as myocarditis. Severe left ventricular dysfunction and biventricular involvement may be associated with a higher likelihood of malignant ventricular tachyarrhythmia.
Authors
- Eric S. Silver (ORCID: https://orcid.org/0000-0002-6092-4462)
- Nak Hyun Choi (ORCID: https://orcid.org/0000-0002-5934-4647)
- Chet Villa (ORCID: https://orcid.org/0000-0002-8195-0694)
- William R. Goodyer (ORCID: https://orcid.org/0000-0002-3252-1180)
- Charles I. Berul (ORCID: https://orcid.org/0000-0002-9604-7369)
- Taylor S. Howard
- Teresa M. Lee (ORCID: https://orcid.org/0000-0001-7409-6832)
- Sara Cherny (ORCID: https://orcid.org/0000-0002-1453-6055)
- Leonardo Liberman (ORCID: https://orcid.org/0000-0002-5492-6584)
- Anna Joong (ORCID: https://orcid.org/0000-0003-2223-0045)
- Warren A. Zuckerman (ORCID: https://orcid.org/0000-0003-3856-7726)
Institutions
- Cincinnati Children's Hospital Medical Center (US)
- Morgan Stanley Children's Hospital (US)
- Children's National (US)
- Palo Alto University (US)
- Lurie Children's Hospital (US)
- Stanford Medicine (US)
- Texas Children's Hospital (US)
- Robert H. Lurie Comprehensive Cancer Center of Northwestern University
- University of Cincinnati Medical Center (US)
- Stanford University (US)
Publication Details
- Journal
- Circulation Arrhythmia and Electrophysiology
- Published
- 2024-11-01
- DOI
- https://doi.org/10.1161/circep.124.013114
- Citations
- 8
- Primary Topic
- Cardiovascular Effects of Exercise
- Type
- article
- Field-Weighted Citation Impact
- 3.22