Homozygous Familial Hypercholesterolemia in Spain: Data From Registry of the Spanish Atherosclerosis Society

The current situation of HoFH in Spain is better than expected, with marked reductions in LDLc levels with new treatments. In this population, recommended LDLc goals are difficult to achieve despite maximum lipid-lowering therapy. ASCVD has been reduced and delayed by 2 decades.

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Publication Details

Journal
The Journal of Clinical Endocrinology & Metabolism
Published
2024-11-08
DOI
https://doi.org/10.1210/clinem/dgae784
Citations
5
Primary Topic
Lipoproteins and Cardiovascular Health
Type
article
Field-Weighted Citation Impact
2.86

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article

Homozygous Familial Hypercholesterolemia in Spain: Data From Registry of the Spanish Atherosclerosis Society

Sergio Martínez‐Hervás, Rosa M. Sánchez-Hernández, L. Masana, Francisco Fuentes et al.
5 citations
The Journal of Clinical Endocrinology & Metabolism
Lipoproteins and Cardiovascular Health
2.86
article

Homozygous Familial Hypercholesterolemia in Spain: Data From Registry of the Spanish Atherosclerosis Society

Sergio Martínez‐Hervás, Rosa M. Sánchez-Hernández, L. Masana, Francisco Fuentes, Agustín Blanco-Echevarría, Fernando Civeira, Begoña Cortés Rodríguez, Rosa Argüeso Armesto, Pablo González‐Bustos, Paula Sánchez Sobrino, Daiana Ibarretxe, Antonio Montes Pérez, Gemma Rodríguez-Carnero, María Mercedes Martín Ordiales
article en
5 citations

Abstract

The current situation of HoFH in Spain is better than expected, with marked reductions in LDLc levels with new treatments. In this population, recommended LDLc goals are difficult to achieve despite maximum lipid-lowering therapy. ASCVD has been reduced and delayed by 2 decades.

The Journal of Clinical Endocrinology & MetabolismVol. 110(8)
Universidad de Las Palmas de Gran Canaria (ES), Universitat Autònoma de Barcelona (ES), Universidad de Zaragoza (ES), Hospital Universitario Insular de Gran Canaria (ES), Hospital de Sant Pau (ES), Centro de Investigación Biomédica en Red Diabetes y Enfermedades Metabólicas Asociadas (ES), Instituto Maimónides de Investigación Biomédica de Córdoba (ES), Hospital Clínico Universitario de Valencia (ES), Centro de Investigación en Red en Enfermedades Cardiovasculares (ES), Complejo Hospitalario Universitario de Santiago (ES), Complejo Hospitalario de Salamanca (ES), Hospital Universitario 12 De Octubre (ES), Institut de Recerca Biomèdica Catalunya Sud (ES), Hospital Universitario Miguel Servet (ES), Centro de Investigación Biomédica en Red (ES), Hospital Universitario Virgen de las Nieves (ES), Hospital Universitario Reina Sofía (ES), Instituto de Investigación Sanitaria Aragón (ES), Complexo Hospitalario Universitario A Coruña (ES), Hospital Universitario Lucus Augusti (ES), Hospital Universitari Sant Joan de Reus (ES), Hospital Montecelo (ES), Universitat Rovira i Virgili (ES)
Ultragenyx Pharmaceutical, Instituto de Salud Carlos III
Good health and well-being
Openalex Percentile: Top 9%
Lipoproteins and Cardiovascular Health
2.86
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