Clinical Features and Outcomes of Pediatric <i>MYH7</i> ‐Related Dilated Cardiomyopathy
Pediatric <i>MYH7</i>-related DCM is characterized by early onset, frequent LV hypertrabeculation, and poor prognosis. Advanced New York Heart Association class and low LV ejection fraction emerged as predictors of end-stage heart failure.
Authors
- Paloma Remior Pérez (ORCID: https://orcid.org/0000-0002-7768-4469)
- Roberto Barriales‐Villa (ORCID: https://orcid.org/0000-0002-6721-3487)
- Georgia Sarquella‐Brugada (ORCID: https://orcid.org/0000-0002-6857-8904)
- Gregory Webster (ORCID: https://orcid.org/0000-0002-9107-8342)
- Fernando de Frutos (ORCID: https://orcid.org/0000-0003-4350-3217)
- Francesca Girolami (ORCID: https://orcid.org/0000-0001-9143-3597)
- Karim Wahbi (ORCID: https://orcid.org/0000-0001-7682-7387)
- Dennis Dooijes (ORCID: https://orcid.org/0000-0003-0312-5354)
- Reyes Álvarez García-Rovés
- Fernándo Domínguez (ORCID: https://orcid.org/0000-0001-8408-363X)
- Miloš Kubánek (ORCID: https://orcid.org/0000-0003-1864-0949)
- María Eugenia Fuentes Cañamero (ORCID: https://orcid.org/0000-0003-1239-1275)
- Martijn G. Slieker (ORCID: https://orcid.org/0000-0001-8198-511X)
- Pablo García‐Pavía (ORCID: https://orcid.org/0000-0002-5470-2257)
- Juan Pablo Ochoa
- María Sabater‐Molina (ORCID: https://orcid.org/0000-0003-1352-1748)
- Dominic James Abrams (ORCID: https://orcid.org/0000-0001-5266-2805)
- Javier Limeres Freire (ORCID: https://orcid.org/0000-0003-3644-9494)
- Sergi César (ORCID: https://orcid.org/0000-0002-2798-1756)
- M. Jansen (ORCID: https://orcid.org/0000-0002-0896-4440)
- Torsten B. Rasmussen (ORCID: https://orcid.org/0000-0003-1468-7248)
Institutions
- Northwestern University (US)
- Universidad Complutense de Madrid (ES)
- Boston Children's Hospital (US)
- Lurie Children's Hospital (US)
- Hospital Sant Joan de Déu Barcelona (ES)
- Harvard University (US)
- Utrecht University (NL)
- Université Paris Cité (FR)
- Universidad Francisco de Vitoria (ES)
- Universitat de Girona (ES)
- Instituto de Salud Carlos III (ES)
- Aarhus University Hospital (DK)
- Spanish National Centre for Cardiovascular Research (ES)
- Hospital General Universitario Gregorio Marañón (ES)
- University Medical Center Utrecht (NL)
- Sorbonne Paris Cité (FR)
- Hôpital Cochin (FR)
- Complejo Hospitalario Universitario de Santiago (ES)
- Hospital Universitario Puerta de Hierro Majadahonda (ES)
- Meyer Children's Hospital (IT)
- Sant Joan de Déu Research Foundation (ES)
- Vall d'Hebron Hospital Universitari (ES)
- Institute of Clinical and Experimental Medicine (CZ)
- Hospital Materno-Infantil (ES)
- Complexo Hospitalario Universitario A Coruña (ES)
- ERN GUARD-Heart (NL)
- Instituto Murciano de Investigación Biosanitaria (ES)
- Istituti di Ricovero e Cura a Carattere Scientifico (IT)
- Instituto de Investigación Biomédica de A Coruña (ES)
- Institut de Recerca Sant Joan de Déu
- Universitat de Barcelona (ES)
- Universidad de Murcia (ES)
Publication Details
- Journal
- Journal of the American Heart Association
- Published
- 2024-11-04
- DOI
- https://doi.org/10.1161/jaha.124.036208
- Citations
- 2
- Primary Topic
- Cardiomyopathy and Myosin Studies
- Type
- article
- Field-Weighted Citation Impact
- 0.80
Funders
- Aarhus Universitet
- Aarhus Universitetshospital
- Universitat de Girona
- Universidad Francisco de Vitoria
- Dutch Cardiovascular Alliance
- European Commission
- Universiteit Utrecht
- Ministerstvo Zdravotnictví Ceské Republiky
- Universidad de Murcia
- Ministerio de Ciencia e Innovación
- Universitat de Barcelona
- Centro Nacional de Investigaciones Cardiovasculares
- Fundació Institut de Recerca Hospital Universitari Vall d’Hebron
- Instituto de Investigación Sanitaria Gregorio Marañón
- Instituto de Salud Carlos III
- European Regional Development Fund