Unilateral retinitis pigmentosa in Von Recklinghausen disease: A rare occurrence

Retinitis pigmentosa (RP) is hereditary progressive retinal dystrophy causing symmetrical affliction of both eyes. Neurofibromatosis 1 (NF1)/Von Recklinghausen disease is a hereditary neurocutaneous disorder with ocular involvement. But, occurrence of retinitis pigmentosa in NF1 is very uncommon, and unilateral RP in this scenario is a rare occurrence. This case report is of a male patient with NF1 presenting with unilateral RP on ophthalmological examination. This case is being presented for its rarity.