Does regression of skin thickening predict improvement of internal organ involvement and survival in patients with diffuse cutaneous systemic sclerosis? A EUSTAR analysis
We found that regression of skin fibrosis is associated with a lower probability of lung progression and better survival at follow up. The link between the disease course of skin and lung fibrosis in SSc can help to better stratify patients in clinical practice and enrich for ILD progressive patients in clinical trials.
Authors
- Maria Üprus
- Carlo Selmi (ORCID: https://orcid.org/0000-0002-0323-0376)
- Vera Ortiz-Santamaría (ORCID: https://orcid.org/0000-0001-6016-606X)
- Luc Mouthon (ORCID: https://orcid.org/0000-0002-7021-9492)
- Petros Paul Sfikakis (ORCID: https://orcid.org/0000-0001-5484-2930)
- Piotr Wiland (ORCID: https://orcid.org/0000-0001-9999-0267)
- Svetlana Agachi
- Ulrich A. Walker (ORCID: https://orcid.org/0000-0002-9183-550X)
- Francesca Ingegnoli (ORCID: https://orcid.org/0000-0002-6727-1273)
- Leland W.K. Chung (ORCID: https://orcid.org/0000-0003-0072-6939)
- Rosario Foti (ORCID: https://orcid.org/0000-0002-7301-8362)
- Srđan Novak (ORCID: https://orcid.org/0000-0001-8870-4704)
- Jörg Henes (ORCID: https://orcid.org/0000-0002-8385-6861)
- Tim Schmeiser (ORCID: https://orcid.org/0000-0001-7342-0020)
- François Spertini (ORCID: https://orcid.org/0000-0002-3256-1377)
- Thierry Zénone
- Florenzo Iannone (ORCID: https://orcid.org/0000-0003-0474-5344)
- Alexandra Balbir‐Gurman (ORCID: https://orcid.org/0000-0003-4694-6099)
- Michele Iudici (ORCID: https://orcid.org/0000-0001-5871-8806)
- Gabriela Riemekasten (ORCID: https://orcid.org/0000-0002-5406-2464)
- Dominique Farge Bancel
- Eric HACHULLA (ORCID: https://orcid.org/0000-0001-7432-847X)
- Francesco Paolo Cantatore (ORCID: https://orcid.org/0000-0001-9929-9177)
- Matthias Seidel (ORCID: https://orcid.org/0000-0003-0861-0869)
- Carlomaurizio Montecucco (ORCID: https://orcid.org/0000-0001-8263-3925)
- Ira Litinsky
- Douglas J. Veale (ORCID: https://orcid.org/0000-0003-2802-4971)
- Lorenzo Dagna (ORCID: https://orcid.org/0000-0002-7428-315X)
- Paloma García de la Peña Lefebvre (ORCID: https://orcid.org/0000-0001-6586-6903)
- Fahrettin Öksel (ORCID: https://orcid.org/0000-0001-5990-9452)
- Elena Rezuş (ORCID: https://orcid.org/0000-0002-8175-2583)
- Ruxandra Ionescu (ORCID: https://orcid.org/0000-0001-7651-0099)
- Ana-Maria Ramazan
- Jörg H. W. Distler (ORCID: https://orcid.org/0000-0001-7408-9333)
- Mohammed Tikly (ORCID: https://orcid.org/0000-0001-7850-3538)
- Kamal Solanki (ORCID: https://orcid.org/0000-0002-2953-9064)
- Bojana Stamenković (ORCID: https://orcid.org/0000-0003-3581-4867)
- Katja Perdan Pirkmajer (ORCID: https://orcid.org/0000-0001-7778-4016)
- Goda Šeškutė (ORCID: https://orcid.org/0000-0003-4830-1497)
- Cord Sunderkötter (ORCID: https://orcid.org/0000-0002-2929-145X)
- Marie‐Elise Truchetet (ORCID: https://orcid.org/0000-0001-8045-0180)
- Alessandro Giollo (ORCID: https://orcid.org/0000-0001-9355-7673)
- Branimir Anić (ORCID: https://orcid.org/0000-0003-4940-0577)
- Jeska de Vries‐Bouwstra
- Dominik Majewski (ORCID: https://orcid.org/0000-0002-7731-5647)
- Carolina de Souza Müller (ORCID: https://orcid.org/0000-0003-1886-0773)
- Simona Rednic (ORCID: https://orcid.org/0000-0001-8149-7722)
- Nicolas Hunzelmann
- Ina Kötter (ORCID: https://orcid.org/0000-0002-9262-005X)
- Yannick Allanore (ORCID: https://orcid.org/0000-0002-6149-0002)
- Bernard Coleiro
- Juan José Alegre Sancho (ORCID: https://orcid.org/0000-0003-1641-0875)
- Suzana Jordan (ORCID: https://orcid.org/0000-0002-8114-8239)
- Susanne Ullman
- Şule Yavuz (ORCID: https://orcid.org/0000-0001-5053-6426)
- Massimiliano Limonta
- Ellen De Langhe
- Ana Maria Gheorghiu (ORCID: https://orcid.org/0000-0002-1292-2964)
- Elise Siegert (ORCID: https://orcid.org/0000-0002-9594-0446)
- Vera Bernardino (ORCID: https://orcid.org/0000-0002-8492-5910)
- Valeria Riccieri (ORCID: https://orcid.org/0000-0002-7507-5483)
- Esthela Loyo
- Kristine Herrmann
- Daniel E. Furst (ORCID: https://orcid.org/0000-0001-7857-2373)
- Stefan Heitmann
- Mengtao Li (ORCID: https://orcid.org/0000-0003-4252-2889)
- Lisa K. Stamp (ORCID: https://orcid.org/0000-0003-0138-2912)
- Francesco Del Galdo (ORCID: https://orcid.org/0000-0002-8528-2283)
- Patricia Esmeralda Carreira (ORCID: https://orcid.org/0000-0001-8279-3806)
- Radim Bečvář (ORCID: https://orcid.org/0000-0003-0022-3135)
- Eugeniusz J. Kucharz (ORCID: https://orcid.org/0000-0001-5571-8114)
- Vanessa Smith
- Codrina Ancuța (ORCID: https://orcid.org/0000-0002-1777-8121)
- Britta Maurer (ORCID: https://orcid.org/0000-0001-9385-8097)
- Cristina-Mihaela Tănăseanu
- Jean Sibilia (ORCID: https://orcid.org/0000-0002-1601-4795)
- Mislav Radić (ORCID: https://orcid.org/0000-0003-0350-6800)
- Eduardo Kerzberg (ORCID: https://orcid.org/0000-0002-5704-6777)
- Piercarlo Sarzi‐Puttini (ORCID: https://orcid.org/0000-0002-8673-5133)
- Nicole Graf (ORCID: https://orcid.org/0000-0003-3608-2071)
- Giovanna Cuomo (ORCID: https://orcid.org/0000-0002-4292-3589)
- Alessandra Vacca (ORCID: https://orcid.org/0000-0003-4289-2548)
- Brigitte Krummel-Lorenz
- Kilian Eyerich (ORCID: https://orcid.org/0000-0003-0094-2674)
- Elisabetta Zanatta (ORCID: https://orcid.org/0000-0002-4845-5413)
- Thierry Martin (ORCID: https://orcid.org/0000-0002-2776-2641)
- Roger Hesselstrand
- Oliver Distler
- Armando Gabrielli (ORCID: https://orcid.org/0000-0003-3189-5516)
- Lesley Ann Saketkoo (ORCID: https://orcid.org/0000-0002-1878-8591)
- Raffaele Pellerito
- Nemanja Damjanov
- László Czirják
- Marco Matucci Cerinic
- Maria João Salvador
- Ulf Müller‐Ladner (ORCID: https://orcid.org/0009-0000-8832-8112)
- L. Ananieva
- Merete Engelhart
- Christopher P. Denton
- Maria Rosa Pozzi
- Annika Wyss
- Simon Stebbings
- A Vold
Institutions
- Marche Polytechnic University (IT)
- Oslo University Hospital (NO)
- University of Leeds (GB)
- University of Padua (IT)
- Radboud University Nijmegen (NL)
- University of Freiburg (DE)
- Medical University of Silesia (PL)
- Chinese Academy of Medical Sciences & Peking Union Medical College (CN)
- University of Zurich (CH)
- Peking Union Medical College Hospital (CN)
- Radboud University Medical Center (NL)
- Ege University (TR)
- Düsseldorf University Hospital (DE)
- University Hospital of Zurich (CH)
- NIHR Leeds Musculoskeletal Biomedical Research Unit (GB)
- Heinrich Heine University Düsseldorf (DE)
- University of Florence (IT)
- Charité - Universitätsmedizin Berlin (DE)
- Sapienza University of Rome (IT)
Publication Details
- Journal
- Arthritis Research & Therapy
- Published
- 2024-10-31
- DOI
- https://doi.org/10.1186/s13075-024-03418-2
- Citations
- 5
- Primary Topic
- Systemic Sclerosis and Related Diseases
- Type
- article
- Field-Weighted Citation Impact
- 2.12
Funders
- Universität Zürich
- Universitätsspital Zürich