An unusual case of left-sided hemitruncus arteriosus associated with aortic arch hypoplasia

Hemitruncus arteriosus patří mezi nejvzĂĄcnějĹĄĂ­ vrozenĂŠ kardiovaskulĂĄrnĂ­ malformace. Obvykle postihuje pravou plicnĂ­ tepnu. Hemitruncus arteriosus se mĹŻĹže vyskytnout buď izolovaně, nebo ve spojenĂ­ s dalĹĄĂ­mi srdečnĂ­mi vadami, jako jsou defekty septa a Fallotova tetralogie; nicmĂŠně se s nĂ­ lze pouze zřídkakdy setkat současně s postiĹženĂ­m aortĂĄlnĂ­ho oblouku. Popisujeme neobvyklĂ˝ případ 15dennĂ­ho novorozence s levostrannĂ˝m hemitruncus arteriosus spojenĂ˝m s hypoplaziĂ­ aortĂĄlnĂ­ho oblouku, koarktacĂ­ aorty, otevřenou tepennou (Botallovou) dučejĂ­ (patent ductus arteriosus) a s kraniofaciĂĄlnĂ­mi abnormalitami, u něhoĹž byla provedena chirurgickĂĄ korekce. © 2024, ČKS.

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Publication Details

Journal
Cor et Vasa
Published
2024-10-25
DOI
https://doi.org/10.33678/cor.2024.035
Primary Topic
Congenital Heart Disease Studies
Type
article
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article

An unusual case of left-sided hemitruncus arteriosus associated with aortic arch hypoplasia

Serap Yücel, Murat Uğurlucan, Emin Tirelı, H Alhashmi et al.
Cor et Vasa
Congenital Heart Disease Studies
article

An unusual case of left-sided hemitruncus arteriosus associated with aortic arch hypoplasia

Serap Yücel, Murat Uğurlucan, Emin Tirelı, H Alhashmi, Didem Melis Öztaş, Hakan Akıllı, Aslan Babayiğit
article en

Abstract

Hemitruncus arteriosus patří mezi nejvzĂĄcnějĹĄĂ­ vrozenĂŠ kardiovaskulĂĄrnĂ­ malformace. Obvykle postihuje pravou plicnĂ­ tepnu. Hemitruncus arteriosus se mĹŻĹže vyskytnout buď izolovaně, nebo ve spojenĂ­ s dalĹĄĂ­mi srdečnĂ­mi vadami, jako jsou defekty septa a Fallotova tetralogie; nicmĂŠně se s nĂ­ lze pouze zřídkakdy setkat současně s postiĹženĂ­m aortĂĄlnĂ­ho oblouku. Popisujeme neobvyklĂ˝ případ 15dennĂ­ho novorozence s levostrannĂ˝m hemitruncus arteriosus spojenĂ˝m s hypoplaziĂ­ aortĂĄlnĂ­ho oblouku, koarktacĂ­ aorty, otevřenou tepennou (Botallovou) dučejĂ­ (patent ductus arteriosus) a s kraniofaciĂĄlnĂ­mi abnormalitami, u něhoĹž byla provedena chirurgickĂĄ korekce. © 2024, ČKS.

Cor et VasaVol. 66(5)
Good health and well-being
Openalex Percentile: Top 71%
Congenital Heart Disease Studies
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