Rare connective tissue diseases in patients with C1-inhibitor deficiency hereditary angioedema: first evidence on prevalence and distribution from a large Italian cohort study
A relevant prevalence of RCTDs is documented in C1INH-HAE patients, mainly SLE. Patients with RCTDs are on LTP in a significant proportion supporting the idea of a bidirectional link between C1INH-HAE and autoimmunity.
Authors
- L. Lo Sardo
- Paola Triggianese (ORCID: https://orcid.org/0000-0002-1954-2825)
- Azzurra Cesoni Marcelli (ORCID: https://orcid.org/0009-0002-8587-2619)
- Raffaele Brancaccio (ORCID: https://orcid.org/0000-0002-0975-6758)
- Angelica Petraroli (ORCID: https://orcid.org/0000-0001-5700-7164)
- Francesco Ruben Giardino (ORCID: https://orcid.org/0000-0003-3293-8936)
- Mauro Cancian (ORCID: https://orcid.org/0000-0003-2246-9144)
- Francesco Arcoleo (ORCID: https://orcid.org/0000-0002-7153-4208)
- Davide Firinu (ORCID: https://orcid.org/0000-0002-5768-391X)
- Emanuela Cataudella
- Donatella Bignardi (ORCID: https://orcid.org/0000-0001-9995-7467)
- Francesca Perego (ORCID: https://orcid.org/0000-0003-3973-6931)
- Riccardo Senter (ORCID: https://orcid.org/0000-0001-7987-8235)
- Antonio Gidaro (ORCID: https://orcid.org/0000-0002-5379-1091)
- Andrea Zanichelli (ORCID: https://orcid.org/0000-0002-7512-4644)
- P Accardo
- Luisa Brussino (ORCID: https://orcid.org/0000-0001-7249-7616)
- Paolina Quattrocchi
- A. Bergamini
- Giuseppe Spadaro (ORCID: https://orcid.org/0000-0001-7889-425X)
- Oliviero Rossi
- Maria Domenica Guarino
Institutions
- University of Messina (IT)
- University of Rome Tor Vergata (IT)
- University of Padua (IT)
- University of Cagliari (IT)
- University of Milan (IT)
- Luigi Sacco Hospital (IT)
- Azienda Sanitaria Unità Locale di Reggio Emilia (IT)
- Istituti Clinici Scientifici Maugeri (IT)
- L'organizzazione Ospedale di Civitanova M (IT)
- Ospedale Vincenzo Cervello (IT)
- IRCCS Policlinico San Donato (IT)
- Azienda Ospedaliero-Universitaria Careggi (IT)
- Federico II University Hospital (IT)
- Policlinico Universitario di Catania (IT)
- Policlinico Tor Vergata (IT)
- Ospedale Policlinico San Martino (IT)
- ASST Fatebenefratelli Sacco (IT)
Publication Details
- Journal
- Frontiers in Immunology
- Published
- 2024-10-18
- DOI
- https://doi.org/10.3389/fimmu.2024.1461407
- Citations
- 5
- Primary Topic
- Coagulation, Bradykinin, Polyphosphates, and Angioedema
- Type
- article
- Field-Weighted Citation Impact
- 2.19