Rare connective tissue diseases in patients with C1-inhibitor deficiency hereditary angioedema: first evidence on prevalence and distribution from a large Italian cohort study

A relevant prevalence of RCTDs is documented in C1INH-HAE patients, mainly SLE. Patients with RCTDs are on LTP in a significant proportion supporting the idea of a bidirectional link between C1INH-HAE and autoimmunity.

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Publication Details

Journal
Frontiers in Immunology
Published
2024-10-18
DOI
https://doi.org/10.3389/fimmu.2024.1461407
Citations
5
Primary Topic
Coagulation, Bradykinin, Polyphosphates, and Angioedema
Type
article
Field-Weighted Citation Impact
2.19
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article

Rare connective tissue diseases in patients with C1-inhibitor deficiency hereditary angioedema: first evidence on prevalence and distribution from a large Italian cohort study

L. Lo Sardo, Paola Triggianese, Azzurra Cesoni Marcelli, Raffaele Brancaccio et al.
5 citations
Frontiers in Immunology
Coagulation, Bradykinin, Polyphosphates, and Angioedema
2.19
article

Rare connective tissue diseases in patients with C1-inhibitor deficiency hereditary angioedema: first evidence on prevalence and distribution from a large Italian cohort study

L. Lo Sardo, Paola Triggianese, Azzurra Cesoni Marcelli, Raffaele Brancaccio, Angelica Petraroli, Francesco Ruben Giardino, Mauro Cancian, Francesco Arcoleo, Davide Firinu, Emanuela Cataudella, Donatella Bignardi, Francesca Perego, Riccardo Senter, Antonio Gidaro, Andrea Zanichelli, P Accardo, Luisa Brussino, Paolina Quattrocchi, A. Bergamini, Giuseppe Spadaro, Oliviero Rossi, Maria Domenica Guarino
article en
5 citations

Abstract

A relevant prevalence of RCTDs is documented in C1INH-HAE patients, mainly SLE. Patients with RCTDs are on LTP in a significant proportion supporting the idea of a bidirectional link between C1INH-HAE and autoimmunity.

Frontiers in ImmunologyVol. 15
University of Messina (IT), University of Rome Tor Vergata (IT), University of Padua (IT), University of Cagliari (IT), University of Milan (IT), Luigi Sacco Hospital (IT), Azienda Sanitaria Unità Locale di Reggio Emilia (IT), Istituti Clinici Scientifici Maugeri (IT), L'organizzazione Ospedale di Civitanova M (IT), Ospedale Vincenzo Cervello (IT), IRCCS Policlinico San Donato (IT), Azienda Ospedaliero-Universitaria Careggi (IT), Federico II University Hospital (IT), Policlinico Universitario di Catania (IT), Policlinico Tor Vergata (IT), Ospedale Policlinico San Martino (IT), ASST Fatebenefratelli Sacco (IT)
Openalex Percentile: Top 12%
Coagulation, Bradykinin, Polyphosphates, and Angioedema
2.19
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