Good cochlear implantation outcomes in subjects with mono-allelic <i>WFS1-</i> associated sensorineural hearing loss – a case series
Individuals with Wolfram-like syndrome or DFNA6/14/38 demonstrate consistently good outcomes following implantation, which remain stable over time. These findings affirm cochlear implantation as an effective rehabilitation option for these individuals. Furthermore, the stable and good CI outcomes contradict the suggested link between <i>WFS1</i>-associated sensorineural hearing loss and auditory neuropathy.
Authors
- Ronald J. E. Pennings (ORCID: https://orcid.org/0000-0001-5517-9683)
- Lonneke Haer‐Wigman (ORCID: https://orcid.org/0000-0003-3595-0797)
- Emmanuel Mylanus
- Wendy J. Huinck (ORCID: https://orcid.org/0000-0003-3479-4657)
- Cris Lanting (ORCID: https://orcid.org/0000-0001-9397-7766)
- M. L. A. Fehrmann (ORCID: https://orcid.org/0000-0002-6995-668X)
Institutions
- Radboud University Nijmegen (NL)
- University Medical Center (US)
- Radboud University Medical Center (NL)
Publication Details
- Journal
- International Journal of Audiology
- Published
- 2024-10-18
- DOI
- https://doi.org/10.1080/14992027.2024.2411579
- Citations
- 1
- Primary Topic
- Hearing, Cochlea, Tinnitus, Genetics
- Type
- article
- Field-Weighted Citation Impact
- 0.36
Funders
- Cochlear