Evaluation of global and regional myocardial work by echocardiography in patients with Fabry disease
Myocardial work analysis can be used to assess global and regional myocardial work in patients with FD. In this study, GLS and GWE were reduced in patients with FD and associated with the presence of LVH. Basal and middle myocardial work decreased in relation to the LVH, while apical myocardial work remained, which added value to explore the distribution of myocardial impairment.
Authors
- Li Yang (ORCID: https://orcid.org/0000-0001-7412-9841)
- Wei Ma (ORCID: https://orcid.org/0000-0003-1305-3980)
- Ying Yang (ORCID: https://orcid.org/0000-0002-8149-1109)
- Yawen Zhao (ORCID: https://orcid.org/0000-0002-7585-3329)
- Wei Zhang (ORCID: https://orcid.org/0000-0002-6385-9846)
- Lin Liu (ORCID: https://orcid.org/0000-0002-1934-1847)
- Han Wang (ORCID: https://orcid.org/0009-0008-1462-649X)
Institutions
- Peking University (CN)
- Peking University First Hospital (CN)
Publication Details
- Journal
- Orphanet Journal of Rare Diseases
- Published
- 2024-10-16
- DOI
- https://doi.org/10.1186/s13023-024-03396-3
- Citations
- 5
- Primary Topic
- Cardiomyopathy and Myosin Studies
- Type
- article
- Field-Weighted Citation Impact
- 2.01
Funders
- National Key Research and Development Program of China