ASSISTÊNCIA DE ENFERMAGEM NA SAÚDE MENTAL DOS PORTADORES DE LINFANGIOLEIOMIOMATOSE

The importance of providing quality and knowledgeable care, and recognizing the impact generated on the mental health of patients with a rare disease, such as Lymphangioleiomyomatosis or LAM, advocating nursing care as essential. Objective: to highlight and inform the need for nursing care in the mental health of patients with LAM. Method: this is a bibliographic review, based on articles selected from the databases: Scientific Electronic Library (SciELO), Brazilian Society of Pulmonology and Tisiology, Google Scholar and the Ministry of Health. The inclusion criteria were articles that were published in the year 2020 to 2024, except for some cases where it was necessary to search for slightly older articles for a more complete research. Results: the nursing team, because it is on the front line of care and has a greater bond with patients, becomes responsible for providing proper care to people who have a rare disease, such as LAM, as this generates psychological illness. Knowing the subject, studying it and providing adequate assistance, thus reducing the impacts generated by this disease. Thus, providing guidance regarding the concept of LAM, the symptoms that may arise, how to reduce them, respecting the entire process and providing the emotional support they need. Conclusion: the presence of a nurse is necessary to provide the appropriate assistance to these patients. It is extremely important to have knowledge of LAM and its harms to the mental health of patients, enabling this professional to be able to provide the best possible care to a patient with a rare disease.