Diagnostic yield of exome sequencing-based copy number variation analysis in Mendelian disorders: a clinical application
Next-generation sequencing (NGS) coupled with bioinformatic tools has revolutionized the detection of copy number variations (CNVs), which are implicated in the emergence of Mendelian disorders. In this study, we evaluated the diagnostic yield of exome sequencing-based CNV analysis in 449 patients with suspected Mendelian disorders. We aimed to assess the diagnostic yield of this recently utilized method and expand the clinical spectrum of intragenic CNVs. The cohort underwent whole exome sequencing (WES) and clinical exome sequencing (CES). Using GATK-gCNV, we identified 12 pathogenic CNVs that correlated with their clinical findings and resulting in a diagnostic yield of 2.67%. Importantly, the study emphasizes the role of CNVs in the etiology of Mendelian disorders and highlights the value of exome sequencing-based CNV analysis in routine diagnostic processes.
Authors
- Asude Durmaz (ORCID: https://orcid.org/0000-0002-4109-9401)
- Esra Işık (ORCID: https://orcid.org/0000-0003-0657-2408)
- Tahir Atık (ORCID: https://orcid.org/0000-0002-1142-3872)
- Seda Kanmaz (ORCID: https://orcid.org/0000-0002-8738-1242)
- Özgür Çoğulu (ORCID: https://orcid.org/0000-0002-9037-5599)
- Melis Köse (ORCID: https://orcid.org/0000-0003-2255-3725)
- Enise Avcı Durmuşalioğlu (ORCID: https://orcid.org/0000-0002-0582-8881)
- Ferda Özkınay (ORCID: https://orcid.org/0000-0001-7542-7787)
- Ayça Aykut (ORCID: https://orcid.org/0000-0002-1460-0053)
Institutions
- Children's Hospital of Philadelphia (US)
- Ege University (TR)
Publication Details
- Journal
- BMC Medical Genomics
- Published
- 2024-09-30
- DOI
- https://doi.org/10.1186/s12920-024-02015-1
- Citations
- 5
- Primary Topic
- Genomic variations and chromosomal abnormalities
- Type
- article
- Field-Weighted Citation Impact
- 2.75