04095 Hormonal treatments in acute hepatic porphyria

area in both median nerves in the forearm, consistent with neural thickening outside typical compression site.Six months later, she presented with psychosis and reported migrainous headache.Brain MRI suggested idiopathic brain hypertension.Lumbar puncture demonstrated increased opening pressure of 32 cmH2O.A new attack was discarded with biochemical exams.Discussion Acute porphyric neuropathy is described as an axonal predominantly motor neuropathy.Secondary demyelinating findings have been described.A primary demyelinating neuropathy and partial conduction block, as seen in our case, have been reported in the acute phase and related to more severe acute attacks.A chronic distal axonal sensory-motor polyneuropathy can persist.Specific ultrasonography features of porphyric neuropathy have not been reported.This unpredicted finding can be a source of misleading diagnosis as inflammatory neuropathy.Finally, intracranial hypertension is not usually seen and further studies are needed to establish a relationship.