Early Diagnosis, Disease Stage and Prognosis in Wild-Type Transthyretin Amyloid Cardiomyopathy: The DIAMOND Study

In this contemporary nationwide cohort, an ATTRwt-CA early diagnosis was very rare. Disease staging with NAC and Columbia scoring systems determined classes of patients with heterogeneous features. Both scores were significantly associated with mortality, but other variables also had prognostic significance.

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Publication Details

Journal
ESC Heart Failure
Published
2024-09-20
DOI
https://doi.org/10.1002/ehf2.15091
Citations
5
Primary Topic
Amyloidosis: Diagnosis, Treatment, Outcomes
Type
article
Field-Weighted Citation Impact
1.17

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article

Early Diagnosis, Disease Stage and Prognosis in Wild-Type Transthyretin Amyloid Cardiomyopathy: The DIAMOND Study

Matteo Serenelli, Stefano Perlini, Federico Guerra, Andrea Foli et al.
5 citations
ESC Heart Failure
Amyloidosis: Diagnosis, Treatment, Outcomes
1.17
article

Early Diagnosis, Disease Stage and Prognosis in Wild-Type Transthyretin Amyloid Cardiomyopathy: The DIAMOND Study

Matteo Serenelli, Stefano Perlini, Federico Guerra, Andrea Foli, Alberto Cipriani, Simone Longhi, Francesca Marzo, Giuseppe Ciliberti, Beatrice Musumeci, Lia Crotti, Roberta Mussinelli, Michele Emdin, Gianfranco Sinagra, Laura De Michieli, Carlotta Mazzoni, Giuseppe Vergaro, Pier Filippo Vianello, Giulia Elena Mandoli, Guerino Giuseppe Varrà, Angelo Giuseppe Caponetti, Federico Perfetto, Mattia Zampieri, Christian Gagliardi, Giuseppe Limongelli, Valeria Rella, Samuela Carigi, Emanuele Barbato, Enrico Monti, Elisa Gardini, Giacomo Tini, Laura Piera Obici, Elisa Merli, Marco Canepa, Elena Biagini, Marco Merlo, Italo Porto, Alessia Argirò, Francesco Cappelli, Giuseppe Palmiero, Michela Bartolotti, Giovanni O. Palladini, Paolo Milani, Giulia Saturi, Matteo Cameli, Margherita Zanoletti, Alberto Aimo, Ludovica De Fazio, Giulia Ricci Lucchi, F Fabris, Gioele Fabbri
article en
5 citations

Abstract

In this contemporary nationwide cohort, an ATTRwt-CA early diagnosis was very rare. Disease staging with NAC and Columbia scoring systems determined classes of patients with heterogeneous features. Both scores were significantly associated with mortality, but other variables also had prognostic significance.

ESC Heart FailureVol. 12(1)
University of Siena (IT), Marche Polytechnic University (IT), University of Padua (IT), University of Trieste (IT), Scuola Superiore Sant'Anna (IT), University of Campania "Luigi Vanvitelli" (IT), University of Ferrara (IT), University of Pavia (IT), GNA University (IN), Azienda Unità Sanitaria Locale Della Romagna (IT), Azienda Ospedaliero-Universitaria Careggi (IT), Azienda USL di Bologna (IT), Ospedale per gli Infermi (IT), University of Campania "Luigi Vanvitelli" (IT), Ospedale Infermi di Rimini (IT), IRCCS Istituto Auxologico Italiano (IT), Azienda-Unita' Sanitaria Locale Di Cesena (IT), Ospedale Monaldi (IT), ERN GUARD-Heart (NL), Ospedale Policlinico San Martino (IT), Policlinico San Matteo Fondazione (IT), Istituti di Ricovero e Cura a Carattere Scientifico (IT), Fondazione Toscana Gabriele Monasterio (IT), Azienda Sanitaria Universitaria Integrata di Trieste (IT), Ospedali Riuniti Umberto I (IT), University of Milano-Bicocca (IT), University of Genoa (IT), Sapienza University of Rome (IT), University of Bologna (IT)
Pfizer
Good health and well-being
Openalex Percentile: Top 22%
Amyloidosis: Diagnosis, Treatment, Outcomes
1.17
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