Hemofilia en urgencias

Introduction: hemophilia is an inherited bleeding disorder in which the blood does not clot properly due to low levels of clotting factors VIII or IX, which can cause spontaneous bleeding. The severity of hemophilia is determined by the amount of factor in the blood. Objective: to identify the main sites of spontaneous bleeding and its complications, which is fundamental for care, prevention, and prognosis in these patients. Methods: a literature search performed in the Pubmed, Access Medina, ClinicalKey and Science Direct databases, between August 23, 2021, and January 2023. Discussion: we describe the complications and main characteristics of hemophilia affected individuals, the clinical manifestations related to hemorrhagic events, and that severity correlates with the blood level of clotting factors, as reported in the literature. Conclusions: both hemophilia A and B are associated with spontaneous bleeding or bleeding following injuries or surgery. Clinical presentations vary depending on the involved systems. Adequate factor replacement therapy helps prevent bleeding episodes and the development of complications.