Twin Pregnancy in Patient With Fontan Circulation and Homozygous MTHFR Mutation

Singleton pregnancy in Fontan patients is burdened by a significant maternal cardiovascular and obstetric risk. The cardiac workload in a twin pregnancy is greater and could place Fontan-palliated patients at an increased risk of complications. We report a case of a woman with Fontan circulation and homozygous <i>MTHFR</i> mutation who had a twin pregnancy.

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Publication Details

Journal
JACC Case Reports
Published
2024-09-01
DOI
https://doi.org/10.1016/j.jaccas.2024.102526
Primary Topic
Cardiovascular Issues in Pregnancy
Type
article
Field-Weighted Citation Impact
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article

Twin Pregnancy in Patient With Fontan Circulation and Homozygous MTHFR Mutation

Maria Lucia Narducci, Veronica Lisignoli, Emanuela Concetta D’Angelo, Rosalinda Palmieri et al.
JACC Case Reports
Cardiovascular Issues in Pregnancy
article

Twin Pregnancy in Patient With Fontan Circulation and Homozygous MTHFR Mutation

Maria Lucia Narducci, Veronica Lisignoli, Emanuela Concetta D’Angelo, Rosalinda Palmieri, Gianfranco Butera, Antonio Lanzone, Giulia Di Già, A. Romiti, Rossella Iuzzolino, Marco Della Porta
article en

Abstract

Singleton pregnancy in Fontan patients is burdened by a significant maternal cardiovascular and obstetric risk. The cardiac workload in a twin pregnancy is greater and could place Fontan-palliated patients at an increased risk of complications. We report a case of a woman with Fontan circulation and homozygous <i>MTHFR</i> mutation who had a twin pregnancy.

JACC Case ReportsVol. 29(18)
Agostino Gemelli University Polyclinic (IT), Bambino Gesù Children's Hospital (IT), Istituti di Ricovero e Cura a Carattere Scientifico (IT)
Openalex Percentile: Top 72%
Cardiovascular Issues in Pregnancy
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