Technique for staged biventricular repair of heterotaxy, double-outlet right ventricle, unbalanced atrioventricular canal defect, and transposition

Heterotaxy syndrome with associated congenital defects such as double-outlet right ventricle (DORV), complete atrioventricular canal (CAVC), and transposition of the great arteries (TGA) presents significant surgical challenges. Traditional management often involves single-ventricle palliation, but advances in surgical techniques have made complex biventricular repair a viable option.1 This Case Report describes the technical aspects of staged biventricular repair in a patient initially deemed unsuitable for such an intervention.