A Case Report of MEN Syndrome Type 1 with Boerhaave’s Syndrome Presenting As Tension Hydropneumothorax

Boerhaave Syndrome is a spontaneous rupture of the esophagus due to repeated vomiting and has a high mortality rate. Multiple endocrine neoplasia(MEN) syndromes are autosomal dominant disorders that can develop tumors in endocrine glands. A male patient in his 40s was admitted to the emergency room with complaints of chronic diarrhea and nausea. The patient was hospitalized in the gastroenterology department with a preliminary diagnosis of acute pancreatitis which was excluded later. On the first day of hospitalization, the patient developed dyspnea with desaturation after repeated retching. Thoracoabdominal CT revealed massive pleural effusion on the right side. Therefore, a chest tube was inserted. Six-hour later, he became hypotensive and a chest X-ray revealed a left-sided pneumothorax. A second chest tube was inserted. He was diagnosed with Boerhaave Syndrome by esophagography. Metallic stent was placed in the ruptured site.He eventually died of sepsis due to mediastinitis due to Boerhaave’s syndrome.