Low-grade fibromyxoid sarcoma and sclerosing epithelioid fibrosarcoma, outcome of advanced disease: retrospective study from the Ultra-Rare Sarcoma Working Group
In this series, the largest available, metastatic LGFMS, SEF, and H-LGFMS/SEF showed different courses. Systemic agents have modest efficacy, informing future trials of novel agents for these tumours.
Authors
- Andrea Napolitano (ORCID: https://orcid.org/0000-0002-7509-1555)
- Andrew J. Wagner (ORCID: https://orcid.org/0000-0002-4384-9448)
- Jonathan C. Trent (ORCID: https://orcid.org/0000-0001-6169-5238)
- Alexander T.J. Lee (ORCID: https://orcid.org/0000-0003-2976-6811)
- Daniel Wong (ORCID: https://orcid.org/0000-0001-5069-1557)
- Carlo María Cicala (ORCID: https://orcid.org/0000-0002-4350-495X)
- Daniel Baumhoer (ORCID: https://orcid.org/0000-0002-2137-7507)
- Ryan A. Denu (ORCID: https://orcid.org/0000-0001-9698-9201)
- Silva Ljevar (ORCID: https://orcid.org/0000-0002-1151-1477)
- Angelo Paolo Dei Tos (ORCID: https://orcid.org/0000-0002-1228-8940)
- Hanna Koseła-Paterczyk (ORCID: https://orcid.org/0000-0003-4008-5435)
- William D. Tap (ORCID: https://orcid.org/0000-0001-7779-2796)
- Vladimir Andelkovic (ORCID: https://orcid.org/0000-0002-1938-875X)
- Herbert H. Loong (ORCID: https://orcid.org/0000-0002-6607-1106)
- Abdulazeez Salawu (ORCID: https://orcid.org/0000-0002-4420-0958)
- Elizabeth A. Connolly (ORCID: https://orcid.org/0000-0002-5579-3728)
- A. Hong (ORCID: https://orcid.org/0009-0009-4067-1478)
- Elizabeth G. Demicco (ORCID: https://orcid.org/0000-0003-4144-8824)
- Rosalba Miceli (ORCID: https://orcid.org/0000-0003-0954-375X)
- Evan Rosenbaum (ORCID: https://orcid.org/0000-0002-7499-1279)
- Robin L. Jones (ORCID: https://orcid.org/0000-0003-4173-3844)
- Alexander J. Lazar (ORCID: https://orcid.org/0000-0002-6395-4499)
- Christopher D.�M. Fletcher (ORCID: https://orcid.org/0000-0002-8053-9537)
- Silvia Stacchiotti (ORCID: https://orcid.org/0000-0002-1742-8666)
- Stefano Taverna (ORCID: https://orcid.org/0000-0003-1871-8662)
- Koichi Ogura (ORCID: https://orcid.org/0000-0001-6956-3117)
- Claudia Giani (ORCID: https://orcid.org/0000-0001-8630-4037)
- Giacomo Giulio Baldi (ORCID: https://orcid.org/0000-0003-0798-7752)
- Alessandro Gronchi (ORCID: https://orcid.org/0000-0002-4703-3534)
- Robert G. Maki (ORCID: https://orcid.org/0000-0002-9853-2528)
- Marta Sbaraglia (ORCID: https://orcid.org/0000-0002-7116-6513)
- Emanuela Palmerini (ORCID: https://orcid.org/0000-0003-3406-6705)
- Antonella Brunello (ORCID: https://orcid.org/0000-0003-2583-5226)
- Judith V.M.G. Bovée (ORCID: https://orcid.org/0000-0003-1155-0481)
- Inga‐Marie Schaefer (ORCID: https://orcid.org/0000-0001-9710-5500)
- Jyoti Bajpai (ORCID: https://orcid.org/0000-0001-7657-3460)
- Zhi Li (ORCID: https://orcid.org/0000-0002-9111-2408)
- Fernando Augusto Batista Campos (ORCID: https://orcid.org/0000-0002-7771-8059)
Institutions
- Brigham and Women's Hospital (US)
- Mount Sinai Hospital (CA)
- The University of Sydney (AU)
- Memorial Sloan Kettering Cancer Center (US)
- The University of Texas MD Anderson Cancer Center (US)
- Harvard University (US)
- National Taiwan University (TW)
- Chinese University of Hong Kong (HK)
- University of Toronto (CA)
- Homi Bhabha National Institute (IN)
- Leiden University Medical Center (NL)
- Princess Alexandra Hospital (AU)
- Sir Charles Gairdner Hospital (AU)
- University Hospital of Basel (CH)
- Princess Margaret Cancer Centre (CA)
- AC Camargo Hospital (BR)
- Istituto Oncologico Veneto (IT)
- Prince of Wales Hospital (CN)
- Dana-Farber Cancer Institute (US)
- Royal Marsden Hospital (GB)
- Istituto Ortopedico Rizzoli (IT)
- Vall d'Hebron Hospital Universitari (ES)
- The Christie NHS Foundation Trust (GB)
- The Maria Sklodowska-Curie National Research Institute of Oncology (PL)
- Istituti di Ricovero e Cura a Carattere Scientifico (IT)
- Fondazione IRCCS Istituto Nazionale dei Tumori (IT)
- Sylvester Comprehensive Cancer Center (US)
- Hospital of Prato (IT)
- Vall d'Hebron Institute of Oncology (ES)
- University of Pennsylvania (US)
Publication Details
- Journal
- ESMO Open
- Published
- 2024-09-01
- DOI
- https://doi.org/10.1016/j.esmoop.2024.103689
- Citations
- 7
- Primary Topic
- Sarcoma Diagnosis and Treatment
- Type
- article
- Field-Weighted Citation Impact
- 2.93
Funders
- Ministero della Salute