Outcomes of Pediatric Liver Transplantation in Glycogen Storage Disease Type 1b—A Single‐Center Experience
Although LT normalizes fasting tolerance in GSD1b and reduces hospital attendance due to infection, morbidity from infection and gastrointestinal manifestations persist. Children in our cohort experienced high rates of rejection necessitating titration of immunosuppression to balance risk of infection against organ rejection. Future studies should investigate whether early introduction of SGLT2 inhibitors post-LT impact morbidity in this group.
Authors
- Lauren Johansen (ORCID: https://orcid.org/0009-0001-0947-577X)
- Anne Daly (ORCID: https://orcid.org/0000-0003-2579-8699)
- Chayarani Kelgeri (ORCID: https://orcid.org/0000-0002-0112-2945)
- Girish Gupte (ORCID: https://orcid.org/0000-0002-9026-1583)
- Vivek Rajasekaran (ORCID: https://orcid.org/0000-0001-6700-1890)
- Steve Kitchen (ORCID: https://orcid.org/0000-0002-6826-8519)
- Saikat Santra (ORCID: https://orcid.org/0000-0002-7497-3556)
- Suresh Vijay (ORCID: https://orcid.org/0009-0003-1713-6705)
- Sreevidya Sreekantam
- Khalid Sharif (ORCID: https://orcid.org/0000-0003-2703-8423)
- Julian Raiman
Institutions
- Birmingham Children's Hospital (GB)
Publication Details
- Journal
- Pediatric Transplantation
- Published
- 2024-08-30
- DOI
- https://doi.org/10.1111/petr.14839
- Citations
- 2
- Primary Topic
- Glycogen Storage Diseases and Myoclonus
- Type
- article
- Field-Weighted Citation Impact
- 0.94