Case Series of Double Chamber Right Ventricle in Ventricular Septal Defect: Should It Be Missed Out?

Double chamber right ventricle is a rare disorder caused by an abnormal muscular bundle that separates the right ventricle into high- and low-pressure chambers. In this case series, we highlighted two cases with various clinical features while having a double chamber right ventricle. The initial case involves an infant who presented with significant symptoms at the age of two. He was diagnosed with a double chamber right ventricle and an outlet ventricular septal defect. Case two is asymptomatic, with the discovery of a double chamber right ventricle at the age of nine during echo follow-up for the underlying ventricular septal defect. This case series demonstrates the importance of monitoring right ventricular obstruction in patients who have an underlying ventricular septal defect, given the tendency to overlook the presence of a double chamber right ventricle.