A multidisciplinary non-invasive approach to monitor response to intravenous immunoglobulin treatment in neurodegenerative Langerhans cell histiocytosis: a real-world study
Using a standardized diagnostic protocol, we demonstrated that IVIG treatment can lead to clinical stabilization or improvement in all pauci-symptomatic patients with an MRI grading of less than 4.
Authors
- Annalisa Tondo (ORCID: https://orcid.org/0000-0003-2784-5487)
- Maria Luisa Coniglio (ORCID: https://orcid.org/0000-0002-3437-5180)
- Renzo Guerrini (ORCID: https://orcid.org/0000-0002-7272-7079)
- Susanna Rizzi (ORCID: https://orcid.org/0000-0002-8856-9722)
- Marzia Mortilla (ORCID: https://orcid.org/0000-0003-4978-6537)
- Ersilia Lucenteforte (ORCID: https://orcid.org/0000-0001-5608-5902)
- Katiuscia Romano
- Irene Trambusti (ORCID: https://orcid.org/0000-0001-8106-8098)
- Elena Sieni (ORCID: https://orcid.org/0000-0002-6192-9812)
- Carmen Barba (ORCID: https://orcid.org/0000-0001-5445-5842)
Institutions
- Meyer Children's Hospital (IT)
- University of Florence (IT)
Publication Details
- Journal
- Frontiers in Immunology
- Published
- 2024-08-16
- DOI
- https://doi.org/10.3389/fimmu.2024.1422802
- Citations
- 3
- Primary Topic
- Histiocytic Disorders and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.98