Ventricular Septal Defect Repair in a Patient with Hydrocephalus

Congenital heart diseases may be associated with different syndromes or anomalies. Congenital hydrocephalus is a rare disease that leads to increased intracranial pressure due to fluid accumulation through obstruction of intracranial aqueduct flow, Arnold Chiari and Dandy–Walker malformations, or abnormally increased fluid production into intracerebral ventricles. Increased intracranial pressure may produce many problems during the anaesthesia for any operation. Moreover, the postoperative period may be complicated by hydrocephalus. In severe cases, shunt replacement may be necessary. The case reported here is a 10-month-old infant with ventricular septal defect repair diagnosed with hydrocephalus and postoperative early follow-up findings.