Pustular mycosis fungoides has a poor outcome: a multicentric clinicopathological and molecular case series
pMF often follows an aggressive course, with a high risk of LCT and shorter survival, even for patients with early-stage disease. Histological pustules at diagnosis of MF might represent an independent poor prognostic factor, to be confirmed by further studies. As pustules are not always identified clinically, pustules found on histology should be mentioned in MF pathology reports and should prompt discussion of closer follow-up.
Authors
- Thibaut Deschamps
- K. Bagny
- M. Beylot‐Barry (ORCID: https://orcid.org/0000-0001-6150-1229)
- S. Oro (ORCID: https://orcid.org/0000-0002-5383-7096)
- Arnaud Chong‐Si‐Tsaon
- A.‐C. Fougerousse (ORCID: https://orcid.org/0000-0002-2850-867X)
- Christophe Bontoux (ORCID: https://orcid.org/0000-0001-5446-6197)
- Anh tuan Nguyen
- S. Dalac (ORCID: https://orcid.org/0000-0002-9101-3119)
- M. Rafaa
- J. Denamps
- Délphine Legoupil (ORCID: https://orcid.org/0000-0002-1194-7668)
- Christophe Attencourt (ORCID: https://orcid.org/0000-0001-9171-3521)
- Romain Dubois
- Marie‐Hélène Aubriot‐Lorton
- É. Sbidian (ORCID: https://orcid.org/0000-0002-1267-5270)
- Helmut Beltraminelli (ORCID: https://orcid.org/0000-0002-8179-1793)
- Sivem Afach (ORCID: https://orcid.org/0000-0003-2791-223X)
- Marine Badrignans
- G. Chaby (ORCID: https://orcid.org/0000-0003-0172-2892)
- Wafa Koubâa
- Stéphane Dalle (ORCID: https://orcid.org/0000-0002-3423-4548)
- Laurent Mortier (ORCID: https://orcid.org/0000-0002-2644-1790)
- Alexis Claudel
- Ibtissam Moustaghfir
- Nicolás Ortonne (ORCID: https://orcid.org/0000-0003-0111-7422)
- С. В. Скрек (ORCID: https://orcid.org/0000-0002-9112-6834)
- Nathalie Cardot‐Leccia (ORCID: https://orcid.org/0000-0001-8192-8545)
- Diana-Laure Mboumba
- M. D’Incan (ORCID: https://orcid.org/0000-0002-6367-4227)
- Fanny Beltzung (ORCID: https://orcid.org/0009-0006-1202-0019)
- Gilles Le Masson
- H. Houda
- B. Balme
Institutions
- Université Claude Bernard Lyon 1 (FR)
- University of Bern (CH)
- Centre National de la Recherche Scientifique (FR)
- Inserm (FR)
- Université Paris-Est Créteil (FR)
- Université Côte d'Azur (FR)
- Hotel Dieu Hospital (CA)
- Centre Hospitalier Universitaire de Bordeaux (FR)
- Centre Hospitalier Universitaire de Nice (FR)
- Centre Hospitalier Universitaire Henri-Mondor (FR)
- Centre de Recherches en Cancérologie de Toulouse (FR)
- Centre Hospitalier Universitaire de La Réunion (RE)
- Universitätsklinik für Neurologie (AT)
- Centre Georges François Leclerc (FR)
- Assistance Publique – Hôpitaux de Paris (FR)
- Institut universitaire du cancer de Toulouse Oncopole (FR)
- Hospices Civils de Lyon (FR)
- Centre Léon Bérard (FR)
- Hôpital Saint-André (FR)
- Centre Hospitalier Sud Francilien (FR)
- Hôpital Nord (FR)
- CHU Dijon Bourgogne (FR)
- Institut de Recherche sur le Cancer et le Vieillissement de Nice (FR)
- Hôpital Cardiologique du Haut-Lévêque (FR)
- Habib hospital Thameur (TN)
- Centre de Recherche en Cancérologie de Lyon (FR)
- Centre Hospitalier Universitaire de Clermont-Ferrand (FR)
- Hôpital d'Instruction des Armées Bégin (FR)
- Hôpitaux Universitaires Henri-Mondor (FR)
- Centre Hospitalier Régional Universitaire de Brest (FR)
- Hôtel-Dieu de Paris (FR)
- Centre Hospitalier de Valence (FR)
- Austrian Society of Dermatology and Venereology (AT)
- Hôpital Pasteur (FR)
- Centre Antoine Lacassagne (FR)
- Hôpital Claude Huriez (FR)
- Institut Mondor de Recherche Biomédicale (FR)
Publication Details
- Journal
- British Journal of Dermatology
- Published
- 2024-08-12
- DOI
- https://doi.org/10.1093/bjd/ljae312
- Primary Topic
- Cutaneous lymphoproliferative disorders research
- Type
- article
- Field-Weighted Citation Impact
- 0.00