Latest Research in Metabolism and Genetic Disorders

20 research papers · 2026 median publication year

Top Research Topics in Metabolism and Genetic Disorders

Highest-Cited Papers

  1. CIDP in Association With CMT : The Importance of Repeated History Taking and Clinical Examination in the Monitoring of Genetic Neuropathy
  2. Ketone metabolism defects in childhood: a spectrum of overlapping presentations and clinical features
  3. Glutaric aciduria type 1 presenting with Parkinsonism with presynaptic dopaminergic dysfunction in an adult female: a case report
  4. Propionic Acidemia: An Ambispective Cohort Study on Phenotypic and Genotypic Characteristics at a Tertiary Center in Vietnam
  5. Disease Progression Curves of Muscular Strength, Motor and Respiratory Muscle Function in Congenital, Childhood, and Adult Forms of Myotonic Dystrophy Type 1
  6. The Effect of Anti-drug Antibodies on the Bioavailability of Alglucosidase Alfa in Classic Infantile Pompe Disease
  7. Biochemical and Clinical Characterization of a Patient with Partial Biotinidase Deficiency Carrying the Rare BTD c.690C>G (p.Phe230Leu) Variant: A Case Report
  8. Intensive Family-Centered Rehabilitation and Motor Outcomes in a Child with Global Developmental Delay: A Case Report
  9. A Registry-Based Perspective of Interventional Clinical Trials for Duchenne Muscular Dystrophy
  10. Neurodevelopmental and neurological features in children with hypochondroplasia
  11. Hypertrophic cardiomyopathy: a genome-wide association meta-analysis and polygenic risk score
  12. Classical Homocystinuria Incidentally Diagnosed Following a Normal Newborn Screening Result
  13. Novel TBX20 Variations Susceptible to Sporadic Atrial Fibrillation
  14. When the Electromyography (EMG) and the Patient Disagree: Unraveling a Motor Neuron Disease Mimic With Small-Fiber Dysfunction
  15. Care Models for the Genetic Evaluation of Dilated Cardiomyopathy at Sites of the DCM Consortium
  16. Phase 3 Randomized Trial Results of DTX401 AAV Gene Therapy for the Treatment of GSDIa
  17. From Guidelines to Practice: Pilot Implementation and Analytical Boundaries of a Focused ADPKD-Spectrum Gene Panel
  18. Histological manifestations of vitamin A toxicity in the liver
  19. Cobalamin‐Related Remethylation Disorders: Pregnancy Outcomes and Prenatal Treatment‐New Cases and a Literature Study
  20. Medical genetics in Indonesia: development, challenges, and future priorities in a diverse middle-income archipelago
Controls
|||
ALL TIME
JAN
FEB
MAR
APR
MAY
JUN
JUL
AUG
SEP
L3 Region - - 2026 Sep Q3

Metabolism and Genetic Disorders

20 papers

Top Topics (10)

Metabolism and Genetic Disorders3
Folate and B Vitamins Research2
Hereditary Neurological Disorders1
Genetic Neurodegenerative Diseases1
Lysosomal Storage Disorders Research1
Biotin and Related Studies1
Neurogenetic and Muscular Disorders Research1
Muscle Physiology and Disorders1
Connective tissue disorders research1
Genetic Associations and Epidemiology1

Top Publications (20)

1.CIDP in Association With CMT : The Importance of Repeated History Taking and Clinical Examination in the Monitoring of Genetic Neuropathy2.Ketone metabolism defects in childhood: a spectrum of overlapping presentations and clinical features3.Glutaric aciduria type 1 presenting with Parkinsonism with presynaptic dopaminergic dysfunction in an adult female: a case report4.Propionic Acidemia: An Ambispective Cohort Study on Phenotypic and Genotypic Characteristics at a Tertiary Center in Vietnam5.Disease Progression Curves of Muscular Strength, Motor and Respiratory Muscle Function in Congenital, Childhood, and Adult Forms of Myotonic Dystrophy Type 16.The Effect of Anti-drug Antibodies on the Bioavailability of Alglucosidase Alfa in Classic Infantile Pompe Disease7.Biochemical and Clinical Characterization of a Patient with Partial Biotinidase Deficiency Carrying the Rare BTD c.690C>G (p.Phe230Leu) Variant: A Case Report8.Intensive Family-Centered Rehabilitation and Motor Outcomes in a Child with Global Developmental Delay: A Case Report9.A Registry-Based Perspective of Interventional Clinical Trials for Duchenne Muscular Dystrophy10.Neurodevelopmental and neurological features in children with hypochondroplasia11.Hypertrophic cardiomyopathy: a genome-wide association meta-analysis and polygenic risk score12.Classical Homocystinuria Incidentally Diagnosed Following a Normal Newborn Screening Result13.Novel TBX20 Variations Susceptible to Sporadic Atrial Fibrillation14.When the Electromyography (EMG) and the Patient Disagree: Unraveling a Motor Neuron Disease Mimic With Small-Fiber Dysfunction15.Care Models for the Genetic Evaluation of Dilated Cardiomyopathy at Sites of the DCM Consortium16.Phase 3 Randomized Trial Results of DTX401 AAV Gene Therapy for the Treatment of GSDIa17.From Guidelines to Practice: Pilot Implementation and Analytical Boundaries of a Focused ADPKD-Spectrum Gene Panel18.Histological manifestations of vitamin A toxicity in the liver19.Cobalamin‐Related Remethylation Disorders: Pregnancy Outcomes and Prenatal Treatment‐New Cases and a Literature Study20.Medical genetics in Indonesia: development, challenges, and future priorities in a diverse middle-income archipelago
AI Navigator

Ask Laika to Summarize, Analyze, and Connect papers live on the map.

Summarize Papers & Methodologies

Extract key findings, datasets, and comparative methods across publications.

Benchmark Rankings & Visual Analytics

Rank top research institutions, authors, funders, topics, and journals by Field-Weighted Citation Impact (FWCI) and paper volume with instant charts.

Connect Distant Disciplines

Bridge topological clusters on the map to find hidden collaborative intersections.